Papillary cystadenocarcinoma

Overview

Papillary cystadenocarcinoma is an extremely rare malignant neoplasm characterized by cysts and papillary endophytic projections. It was first defined in 1991 by WHO. We presented a case of papillary cystadenocarinoma arising from the submandibular gland in a 78-year-old male patient, and discussed the clinical, histopathological and treatment features of this rare entity in the light of the current literature. Papillary cystadenocarcinoma is an extremely rare malignant neoplasm that was first defined in 1991 by WHO. It has also been called malignant papillary cystadenoma, low-grade papillary adenocarcinoma, or mucus-producing adenopapillary carcinoma. In this article, we report an unusual case of papillary cystadenocarcinoma arising from the submandibular gland.

Symptoms

The present case had no history, signs and symptoms of a primary adenocarcinoma focus in the body.

Diagnosis

The differential diagnosis of papillary cystadenocarcinoma includes adenocarcinoma, salivary duct carcinoma, polymorphous low-grade adenocarcinoma, and metastatic papillary carcinomas.